Isolated left ventricular non-compaction: an unusual indication for heart transplantation.

نویسندگان

  • Katherine Y Y Fan
  • Carmen W S Chan
  • L C Cheng
  • Ryan L Y Ko
  • Y M Lam
  • M H Jim
  • Timmy W K Au
  • Cally K L Ho
  • E P Wang
  • Elaine M C Chau
  • W H Chow
چکیده

We report a patient with isolated left ventricular non-compaction diagnosed by echocardiography and cardiac magnetic resonance imaging. She developed refractory congestive heart failure and subsequently underwent successful heart transplantation. This type of cardiomyopathy is thought to be caused by the arrest of normal embryogenesis of the endocardium and myocardium. The spectrum of clinical, radiological, and pathological abnormalities is discussed.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Isolated left ventricular non-compaction as an unusual cause of heart failure: a case report

INTRODUCTION Isolated left ventricular non-compaction is a recently described form of cardiomyopathy that is associated with a significant risk of life-threatening arrhythmia and thromboembolic complications. CASE PRESENTATION We report the presentation, diagnosis and management of isolated left ventricular non-compaction in a 54-year-old Caucasian woman presenting with progressive symptoms o...

متن کامل

سری موارد کاردیومیوپاتی Non compaction ایزوله بطن چپ

Isolated non compaction of left ventricular myocardium is a rare cardiomyopathy due to abnormalendomyocardialmorphogenesis. The incidence of non compaction cardiomyopathy in the general population has been estimated at 0.05% to 0.25% per year. NCCMP is a heart muscle disorder that is still little known among physicians and was first described in 1984 by engberding and bender. Echocardiograph...

متن کامل

Isolated left ventricular non-compaction in Africa: elucidating myths

We read with great interest the article by Falase et al. in the November 2012 issue of this journal. They stated that there are no documented cases of left ventricular non-compaction in Africa. Furthermore, they propose that this is due to a lack of awareness of this condition among African cardiologists. The purpose of this letter is to highlight that this statement is not entirely accurate. I...

متن کامل

An unusual case of isolated non-compacted right ventricular myocardium.

Isolated ventricular non-compaction is a rare type of cardiomyopathy resulting from arrested myocardial development during embryogenesis. This rare entity can be easily diagnosed by characteristic appearance of prominent myocardial trabeculations and deep inter-trabecular spaces. The clinical manifestations include heart failure signs, ventricular arrhythmias, and cardio-embolic events. Althoug...

متن کامل

A rare case of heterotaxy and left ventricular non-compaction in an adult

Heterotaxy syndrome with left ventricular non-compaction is a rare co-existence of abnormalities with unknown cause. It can be isolated with no other associations, or associated with congenital heart diseases, or it can occur with multiple other congenital abnormalities. We describe the third reported case of heterotaxy syndrome with left ventricular non-compaction presenting in an adult.

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • Hong Kong medical journal = Xianggang yi xue za zhi

دوره 15 5  شماره 

صفحات  -

تاریخ انتشار 2009